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gene_symbol:GATM
Synonyms:AGAT; AT; CCDS3
clone_name:OTI1C9
immunogen:Full length human recombinant protein of human GATM(NP_001473) produced in HEK293 cell.
predicted_size:44.2 kDa
background:This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by mental retardation, language impairment, and behavioral disorders. [provided by RefSeq]
buffer:PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
purification:Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
isotype:IgG1
host:Mouse
applications:FC, IF, IHC, WB
Recommend Dilution:WB 1:500~2000, IHC 1:150, IF 1:100, FLOW 1:100
reactivities:Human, Mouse, Rat
storage:Store at -20°C as received.
gene_symbol:GATM
Synonyms:AGAT; AT; CCDS3
clone_name:OTI1C9
immunogen:Full length human recombinant protein of human GATM(NP_001473) produced in HEK293 cell.
predicted_size:44.2 kDa
background:This gene encodes a mitochondrial enzyme that belongs to the amidinotransferase family. This enzyme is involved in creatine biosynthesis, whereby it catalyzes the transfer of a guanido group from L-arginine to glycine, resulting in guanidinoacetic acid, the immediate precursor of creatine. Mutations in this gene cause arginine:glycine amidinotransferase deficiency, an inborn error of creatine synthesis characterized by mental retardation, language impairment, and behavioral disorders. [provided by RefSeq]
buffer:PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
purification:Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
isotype:IgG1
host:Mouse
applications:FC, IF, IHC, WB
Recommend Dilution:WB 1:500~2000, IHC 1:150, IF 1:100, FLOW 1:100
reactivities:Human, Mouse, Rat
storage:Store at -20°C as received.