商品介绍

gene_symbol：HMBS
Synonyms：PBG-D; PBGD; PORC; UPS
clone_name：OTI5B11
immunogen：Full length human recombinant protein of human HMBS (NP_000181) produced in HEK293T cell.
predicted_size：39.1 kDa
background：This gene encodes a member of the hydroxymethylbilane synthase superfamily. The encoded protein is the third enzyme of the heme biosynthetic pathway and catalyzes the head to tail condensation of four porphobilinogen molecules into the linear hydroxymethylbilane. Mutations in this gene are associated with the autosomal dominant disease acute intermittent porphyria. Alternatively spliced transcript variants encoding different isoforms have been described. [provided by RefSeq, Jul 2008]
buffer：PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
purification：Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
isotype：IgG1
host：Mouse
applications：WB
Recommend Dilution：WB 1:2000
reactivities：Human, Mouse, Rat
storage：Store at -20°C as received.