商品介绍

gene_symbol：ACADM
Synonyms：ACAD1; MCAD; MCADH
clone_name：OTI2G7
immunogen：Full length human recombinant protein of human ACADM (NP_000007) produced in HEK293T cell.
predicted_size：46.59 kDa
background：This gene encodes the medium-chain specific (C4 to C12 straight chain) acyl-Coenzyme A dehydrogenase. The homotetramer enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Defects in this gene cause medium-chain acyl-CoA dehydrogenase deficiency, a disease characterized by hepatic dysfunction, fasting hypoglycemia, and encephalopathy, which can result in infantile death. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq, Jul 2008]
buffer：PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
purification：Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
isotype：IgG1
host：Mouse
applications：IHC, WB
Recommend Dilution：WB 1:2000, IHC 1:500
reactivities：Human, Mouse, Rat
storage：Store at -20°C as received.