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gene_symbol:Frataxin
Synonyms:CyaY; FA; FARR; FRDA; X25
clone_name:OTI1F2
immunogen:Full length human recombinant protein of human FXN(NP_000135) produced in HEK293T cell.
predicted_size:18.8 kDa
background:This nuclear gene encodes a mitochondrial protein which belongs to FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA results in Friedreich ataxia. Alternative splicing results in multiple transcript variants. [provided by RefSeq]
buffer:PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
purification:Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
isotype:IgG1
host:Mouse
applications:FC, WB
Recommend Dilution:WB 1:2000, FLOW 1:100
reactivities:Human
storage:Store at -20°C as received.
gene_symbol:Frataxin
Synonyms:CyaY; FA; FARR; FRDA; X25
clone_name:OTI1F2
immunogen:Full length human recombinant protein of human FXN(NP_000135) produced in HEK293T cell.
predicted_size:18.8 kDa
background:This nuclear gene encodes a mitochondrial protein which belongs to FRATAXIN family. The protein functions in regulating mitochondrial iron transport and respiration. The expansion of intronic trinucleotide repeat GAA results in Friedreich ataxia. Alternative splicing results in multiple transcript variants. [provided by RefSeq]
buffer:PBS (pH 7.3) containing 1% BSA, 50% glycerol and 0.02% sodium azide.
purification:Purified from mouse ascites fluids or tissue culture supernatant by affinity chromatography (protein A/G)
isotype:IgG1
host:Mouse
applications:FC, WB
Recommend Dilution:WB 1:2000, FLOW 1:100
reactivities:Human
storage:Store at -20°C as received.